Abstract : Anti-p200 pemphigoid is a rare autoimmune subepidermal blistering disease, first described in 1996.1 This disorder was initially considered as a more benign condition compared with bullous pemphigoid and epidermolysis bullosa acquisita, but in a recent series of patients, heterogeneous clinical presentations have been described, including cases with a more severe course than previously reported.2 We describe a case with a highly active disease in a heart transplant patient who experienced a dramatic and complete remission after 1 cycle of rituximab.
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Submitted on : Thursday, May 3, 2018 - 2:52:38 PM Last modification on : Thursday, January 14, 2021 - 11:17:12 AM Long-term archiving on: : Monday, September 24, 2018 - 7:08:42 PM
Lisa Rousseau, Catherine Droitcourt, Nolwenn Ropars, Bernard Lelong, Clémence Saillard, et al.. Successful treatment of severe anti-p200 pemphigoid in a heart transplant recipient with a single cycle of rituximab. JAAD Case reports, Elsevier, 2017, 3 (3), pp.175-177. ⟨10.1016/j.jdcr.2017.01.028⟩. ⟨hal-01518892⟩