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Journal articles
Portal vein leiomyosarcoma A rare case of hepatic hilar tumor with review of the literature
Abstract : Portal vein leiomyosarcoma (LMS) is a very rare entity with poor prognosis. Only few cases have been reported in the literature. We report the case of a 53-year-old man with portal vein LMS presenting as a hilar tumor and causing cholestasis. The tumor measured 10 cm and was responsible for right portal vein thrombosis and compression of the biliary convergence. A right hepatectomy with hilar en bloc resection was performed with portal vein and biliary reconstruction. Pathology confirmed the complete resection of a well-differentiated leiomyosarcoma of the portal vein. The postoperative outcome was uneventful and the patient received no adjuvant treatment. Six months after the procedure, the patient is doing well with a normal quality of life and without any sign of recurrence. Aggressive and radical surgery should be proposed in first intention for the treatment of portal vein LMS.
https://hal-univ-rennes1.archives-ouvertes.fr/hal-02115614
Contributor : Laurent Jonchère Connect in order to contact the contributor
Submitted on : Tuesday, April 30, 2019 - 1:37:38 PM
Last modification on : Monday, September 13, 2021 - 3:24:02 PM
Contributor : Laurent Jonchère Connect in order to contact the contributor
Submitted on : Tuesday, April 30, 2019 - 1:37:38 PM
Last modification on : Monday, September 13, 2021 - 3:24:02 PM